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Cardiological Signs and Symptoms in Friedreich's Ataxia

Published online by Cambridge University Press:  18 September 2015

M. Cote ,
A. Davignon ,
K. Pecko-Drouin ,
A. Solignac ,
G. Geoffroy ,
B. Lemieux  and
A. Barbeau
M. Cote
Affiliation:
Centre Hospitalier Universitaire de Sherbrooke, theHôpital Ste-Justine in Montreal, the Hopital Hotel-Dieu in Montreal and the Clinical Research Institute of Montreal
A. Davignon
Affiliation:
Centre Hospitalier Universitaire de Sherbrooke, theHôpital Ste-Justine in Montreal, the Hopital Hotel-Dieu in Montreal and the Clinical Research Institute of Montreal
K. Pecko-Drouin
Affiliation:
Centre Hospitalier Universitaire de Sherbrooke, theHôpital Ste-Justine in Montreal, the Hopital Hotel-Dieu in Montreal and the Clinical Research Institute of Montreal
A. Solignac
Affiliation:
Centre Hospitalier Universitaire de Sherbrooke, theHôpital Ste-Justine in Montreal, the Hopital Hotel-Dieu in Montreal and the Clinical Research Institute of Montreal
G. Geoffroy
Affiliation:
Centre Hospitalier Universitaire de Sherbrooke, theHôpital Ste-Justine in Montreal, the Hopital Hotel-Dieu in Montreal and the Clinical Research Institute of Montreal
B. Lemieux
Affiliation:
Centre Hospitalier Universitaire de Sherbrooke, theHôpital Ste-Justine in Montreal, the Hopital Hotel-Dieu in Montreal and the Clinical Research Institute of Montreal
A. Barbeau*
Affiliation:
Centre Hospitalier Universitaire de Sherbrooke, theHôpital Ste-Justine in Montreal, the Hopital Hotel-Dieu in Montreal and the Clinical Research Institute of Montreal
*
Clinical Research Institute of Montreal, 110 Pine Avenue West, Montreal, H2W 1R7 Quebec, Canada
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Summary:

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The cardiovascular signs and symptoms were recorded in 36 patients with typical Friedreich's Ataxia (Group la, lb). Seventeen patients were asymptomatic and this did not correlate with the severity of the disease. No pathognomonic clinical constellation was found to reveal the underlying cardiomyopathy.

Type
Quebec Cooperative Study of Friedreich's Ataxia
Information
Canadian Journal of Neurological Sciences , Volume 3 , Issue 4 , November 1976 , pp. 319 - 321
Copyright
Copyright © Canadian Neurological Sciences Federation 1976

References

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