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Klinefelter syndroom en psychiatrische stoornissen: Twee gevalsbeschrijvingen en een literatuuroverzicht

Published online by Cambridge University Press:  18 September 2015

P.J.S. Michielsen ,
W.M.A. Verhoeven  and
C.V. de Blécourt
P.J.S. Michielsen
Affiliation:
Respectievelijk arts-assistent, zenuwarts/A-opleider en psychiater/plaatsvervangend A-opleider bij het Vincent van Gogh Instituut voor Psychiatrie, Venray
W.M.A. Verhoeven*
Affiliation:
Respectievelijk arts-assistent, zenuwarts/A-opleider en psychiater/plaatsvervangend A-opleider bij het Vincent van Gogh Instituut voor Psychiatrie, Venray Bijzonder hoogleraar Faculteit der Geneeskunde en Gezondheidswe-tenschappen, Erasmus Universiteit, Rotterdam
C.V. de Blécourt
Affiliation:
Respectievelijk arts-assistent, zenuwarts/A-opleider en psychiater/plaatsvervangend A-opleider bij het Vincent van Gogh Instituut voor Psychiatrie, Venray
*
Vincent van Gogh Instituut voor Psychiatrie, Stationsweg 46, 5803 AC Venray, The Netherlands
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Summary

Klinefelter syndrome is a genetically determined disorder characterized by an additional X-chromosome. Apart from the phenotypical features, the literature about this disorder mentiones a psychopathological phenotype comprising mainly psychoses, depressive diseases and personality disorders. A substantial number of patients presents with mild to moderate mental retardation.

In this paper, two case reports are described and their psychopathology is compared with the data from the existing literature.

Keywords

Klinefelter syndromepsychopathological phenotype
Type
Articles
Information
Acta Neuropsychiatrica , Volume 13 , Issue 1 , March 2001 , pp. 15 - 20
Copyright
Copyright © Scandinavian College of Neuropsychopharmacology 2001

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References

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