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Chapter 14 - Muscular Dystrophy

Published online by Cambridge University Press:  30 November 2019

By
Jamie W. Sinton
Edited by
Adam C. Adler ,
Arvind Chandrakantan  and
Ronald S. Litman
Adam C. Adler
Affiliation:
Texas Children's Hospital
Arvind Chandrakantan
Affiliation:
Texas Children's Hospital
Ronald S. Litman
Affiliation:
The Children's Hospital of Philadelphia
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Summary

This chapter provides a brief review of anesthetic considerations present in patients with suspected and diagnosed muscular dystrophy.The disease presentation, genetics and clinical manifestations are considered. The chapter provides detailed consideration regarding the preoperative work-up and anesthetic considerations for patients with muscular dystrophy.

Keywords

Muscular dystrophyDuchenne muscular dystrophyBecker’s muscular dystrophydilated cardiomyopathyhyperkalemia
Type
Chapter
Information
Case Studies in Pediatric Anesthesia , pp. 64 - 67
Publisher: Cambridge University Press
Print publication year: 2019

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References

Suggested Reading

Kako, H, Corridore, M, Kean, J, et al. Dexmedetomidine and ketamine for sedation for muscle biopsies in patients with Duchenne muscular dystrophy. Paediatr Anaesth. 2014;24(8):851–6. PMID: 24646124.CrossRefGoogle ScholarPubMed
Larach, MG, Brandom, BW, Allen, GC, et al. Malignant hyperthermia deaths related to inadequate temperature monitoring, 2007-2012: A report from the North American Malignant Hyperthermia Registry of the Malignant Hyperthermia Association of the United States. Anesth Analg. 2014;119(6):1359–66. PMID: 25268394.CrossRefGoogle ScholarPubMed
Nigro, G, Comi, LI, Politano, CL, et al. The incidence and evolution of cardiomyopathy in Duchenne muscular dystrophy. Int J Cardiol. 1990;26:271–7. PMID: 2312196.CrossRefGoogle ScholarPubMed
Shapiro, F, Athiraman, U, Clendenin, DJ, et al. Anesthetic management of 877 pediatric patients undergoing muscle biopsy for neuromuscular disorders: a 20 year review. Paediatr Anaesth. 2016;26(7):710–21. PMID: 27111691.CrossRefGoogle ScholarPubMed
Thrush, PT, Allen, HD, Viollet, L, et al. Re-examination of the electrocardiogram in boys with Duchenne muscular dystrophy and correlation with its dilated cardiomyopathy. Am J Cardiol. 2009;103(2):262–5. PMID: 19121448.CrossRefGoogle ScholarPubMed

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