Book contents
- Frontmatter
- Contents
- List of contributors
- Preface
- Acknowledgment
- Section 1 Head and neck
- Case 1 Trilateral retinoblastoma
- Case 2 Fibromatosis colli
- Case 3 Craniopharyngioma
- Case 4 Labyrinthitis ossificans
- Case 5 Branchio-oto-renal syndrome
- Case 6 Medulloblastoma
- Case 7 Ectopic cervical thymus
- Case 8 X-linked adrenoleukodystrophy
- Case 9 Langerhans cell histiocytosis
- Case 10 PHACES syndrome (Posterior fossa malformations, Hemangiomas of the face, Arterial anomalies, Cardiovascular anomalies, Eye anomalies, and Sternal defects or supraumbilical raphe)
- Section 2 Thoracic imaging
- Section 3 Cardiac imaging
- Section 4 Vascular and interventional
- Section 5 Gastrointestinal imaging
- Section 6 Urinary imaging
- Section 7 Endocrine - reproductive imaging
- Section 8 Fetal imaging
- Section 9 Musculoskeletal imaging
- Index
- References
Case 9 - Langerhans cell histiocytosis
from Section 1 - Head and neck
Published online by Cambridge University Press: 05 June 2014
- Frontmatter
- Contents
- List of contributors
- Preface
- Acknowledgment
- Section 1 Head and neck
- Case 1 Trilateral retinoblastoma
- Case 2 Fibromatosis colli
- Case 3 Craniopharyngioma
- Case 4 Labyrinthitis ossificans
- Case 5 Branchio-oto-renal syndrome
- Case 6 Medulloblastoma
- Case 7 Ectopic cervical thymus
- Case 8 X-linked adrenoleukodystrophy
- Case 9 Langerhans cell histiocytosis
- Case 10 PHACES syndrome (Posterior fossa malformations, Hemangiomas of the face, Arterial anomalies, Cardiovascular anomalies, Eye anomalies, and Sternal defects or supraumbilical raphe)
- Section 2 Thoracic imaging
- Section 3 Cardiac imaging
- Section 4 Vascular and interventional
- Section 5 Gastrointestinal imaging
- Section 6 Urinary imaging
- Section 7 Endocrine - reproductive imaging
- Section 8 Fetal imaging
- Section 9 Musculoskeletal imaging
- Index
- References
Summary
Imaging description
A 10-year-old boy presented with pain and soft tissue swelling of the left cheek. A CT scan demonstrated an extensive soft tissue mass centered in the left maxilla with associated cortical erosion of the left alveolar ridge and left maxillary sinus walls. Contralateral involvement of the right alveolar ridge and anterior maxillary sinus wall was also noted. Several teeth appeared to be “floating” within the maxilla. There was absence of adjacent soft tissue fat stranding (Fig. 9.1a–c).
A five-month-old infant presented with bi-parietal scalp swelling. CT of the head showed bi-parietal calvarial lytic lesions with associated soft tissue masses and a characteristic “beveled edge” appearance with greater destruction of the outer table of the calvarium relative to the inner table (Fig. 9.2a, b). On MRI, mixed T1 and T2 intensities and heterogeneous enhancement of the soft tissue mass was seen (Fig. 9.2c–e).
Langerhans cell histiocytosis (LCH) was confirmed pathologically in both cases.
- Type
- Chapter
- Information
- Pearls and Pitfalls in Pediatric ImagingVariants and Other Difficult Diagnoses, pp. 25 - 29Publisher: Cambridge University PressPrint publication year: 2014