Paget’s disease of bone is a common disorder of unresolved etiology characterized by excessive bone resorption followed by excessive bone formation. If the skull isaffected this may result in hearing loss and eventually develop into profound deafness. To date, no cases of cochlear implantation in patients with Paget’s disease have been reported.

The authors present a case of radiographically confirmed Paget’s disease of the skull in a 77-year-old man with a 20-year history of progressive bilateral sensorineural hearing losswho underwent cochlear implantation. A successful insertion of the Nucleus 24 Contour electrodearray was achieved without surgical and postoperative complications.

At the 10 months’ postoperative evaluation, the patient had gained useful open-set speech perception. In quiet conditions, his performance scores on the word and sentence recognition tests were 100 and 98 per cent, respectively. In the presence of noise (at +10 dB. signal-to-noise ratio), his performance scores on the word and sentence recognition tests were 96 and 94per cent, respectively.

Osteoma is the commonest benign tumour of the paranasal sinuses (Handousa, 1952). A case of a large osteoma removed from the frontal and ethmoid sinuses is presented. Histopathological examination of this tumour revealed evidence of bony remodelling similar to that seen in Pagets' disease which has not been previously reported. The pathological significance of this finding is discussed.