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Side selection for cochlear implantation in a case of Cogan's syndrome

Published online by Cambridge University Press:  25 May 2007

Abstract

Cogan's syndrome is a rare clinical entity that is characterised by non-syphilitic interstitial keratitis and audiovestibular symptoms. The cause of Cogan's syndrome is considered to be autoimmune disease, which is supported by the resolution of hearing loss after steroid treatment, and the association with other autoimmune diseases. The sensorineural hearing loss of Cogan's syndrome is progressive over a few months, and sudden, bilateral deafness often occurs, which may be an indication for cochlear implantation. This paper presents the case of a young woman suffering from Cogan's syndrome and sudden, bilateral deafness. With reference to this case, we describe problems regarding cochlear implantation for Cogan's syndrome and radiological findings aiding selection of cochlear implantation side.

Type
Research Article
Copyright
Copyright © JLO (1984) Limited 2007

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References

1 Cogan, D. Syndrome of nonsyphilitic interstitial keratitis and vestibuloauditory symptoms. Arch Ophthalmol 1945;33:144–9Google Scholar
2 Ndiaye, IC, Rassi, SJ, Wiener-Vacher, SR. Cochleovestibular impairment in pediatric Cogan's syndrome. Pediatrics 2002;109:E38CrossRefGoogle ScholarPubMed
3 Garcia, Berrocal JR, Vargas, JA, Vaquero, M, Ramon, y Cajal, S, Ramirez-Camacho, RA. Cogan's syndrome: an oculo-audiovestibular disease. Postgrad Med J 1999;75:262–4Google Scholar
4 Haynes, BF, Kaiser-Kupfer, MI, Mason, P, Fauci, AS. Cogan syndrome: studies in thirteen patients, long-term follow-up, and a review of the literature. Medicine (Baltimore) 1980;59:426–41CrossRefGoogle Scholar
5 Grasland, A, Pouchot, J, Hachulla, E, Bletry, O, Papo, T, Vinceneux, P. Typical and atypical Cogan's syndrome: 32 cases and review of the literature. Rheumatology (Oxford) 2004;43:1007–15CrossRefGoogle ScholarPubMed
6 Helmchen, C, Arbusow, V, Jager, L, Strupp, M, Stocker, W, Schulz, P. Cogan's syndrome: clinical significance of antibodies against the inner ear and cornea. Acta Otolaryngol 1999;119:528–36Google ScholarPubMed
7 Casselman, JW, Majoor, MH, Albers, FW. MR of the inner ear in patients with Cogan syndrome. AJNR Am J Neuroradiol 1994;15:131–8Google ScholarPubMed
8 Pasanisi, E, Vincenti, V, Bacciu, A, Guida, M, Berghenti, T, Barbot, A et al. Cochlear implantation and Cogan syndrome. Otol Neurotol 2003;24:601–4CrossRefGoogle ScholarPubMed
9 Cinamon, U, Kronenberg, J, Hildesheimer, M, Taitelbaum, R. Cochlear implantation in patients suffering from Cogan's syndrome. J Laryngol Otol 1997;111:928–30CrossRefGoogle ScholarPubMed
10 Minet, M, Deggouj, N, Gersdorff, M. Cochlear implantation in patients with Cogan's syndrome: a review of four cases. Eur Arch Otorhinolaryngol 1997;254:459–62CrossRefGoogle ScholarPubMed
11 Tinling, SP, Colton, J, Brodie, HA. Location and timing of initial osteoid deposition in postmeningitic labyrinthitis ossificans determined by multiple fluorescent labels. Laryngoscope 2004;114:675–80CrossRefGoogle ScholarPubMed