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Selexipag use for paediatric pulmonary hypertension: a single centre report focussed on congenital heart disease patients

Part of: Tetralogy of Fallot (TOF) Functionally Univentricular Heart Basic Science Atrial Septal Defect (ASD)

Published online by Cambridge University Press:  30 March 2021

Alvaro Lafuente-Romero Open the ORCID record for Alvaro Lafuente-Romero [Opens in a new window]  and
Alejandro Rodriguez Ogando
Alvaro Lafuente-Romero
Affiliation:
Pediatric Cardiology Section, “Gregorio Marañon” General University Hospital, Madrid, Spain
Alejandro Rodriguez Ogando
Affiliation:
Pediatric Cardiology Section, “Gregorio Marañon” General University Hospital, Madrid, Spain
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Abstract

Pulmonary hypertension is a rare and complex disease with poor prognosis. Paediatric cases are infrequent and usually associated with congenital heart disease. Management is problematical due to the limited therapy available and poor evidence of efficacy. Recently a new medication, selexipag (UptraviR), a prostacyclin receptor agonist, has been approved for the treatment of pulmonary artery hypertension in adults. We report our experience using selexipag in four paediatric patients with pulmonary hypertension associated with congenital heart disease.

Keywords

Pulmonary arterial hypertensionselexipagprostacyclincongenital heart defects
Type
Brief Report
Information
Cardiology in the Young , Volume 31 , Issue 9 , September 2021 , pp. 1513 - 1515
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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