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Idiopathic pulmonary arterial hypertension with coexisting CHD

Published online by Cambridge University Press:  10 January 2018

Thomas G. Day Open the ORCID record for Thomas G. Day [Opens in a new window] ,
Marina Hughes  and
Bejal Pandya
Thomas G. Day*
Affiliation:
Department of Cardiology, Great Ormond Street Hospital for Children NHS Foundation Trust, London, UK Department of Adult Congenital Cardiology, Bart’s Heart Centre, Bart’s Health NHS Trust, London, UK
Marina Hughes
Affiliation:
Department of Cardiology, Great Ormond Street Hospital for Children NHS Foundation Trust, London, UK
Bejal Pandya
Affiliation:
Department of Adult Congenital Cardiology, Bart’s Heart Centre, Bart’s Health NHS Trust, London, UK
*
Author for correspondence: Thomas G. Day, Department of Cardiology, Great Ormond Street Hospital for Children NHS Foundation Trust, London, United Kingdom. Tel: 07944326254; E-mail: [email protected]
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Abstract

Sinus venosus atrial septal defect can result in an increase in pulmonary blood flow and vascular resistance, leading to pulmonary hypertension. Rarely, the degree of pulmonary hypertension is out of proportion to the degree of intra-cardiac shunting. This case outlines the differences between pulmonary hypertension secondary to CHD and idiopathic pulmonary hypertension, and illustrates the investigation and management strategy used in a patient with features of both.

Keywords

Pulmonary hypertensionadult CHDatrial septal defect
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 5 , May 2018 , pp. 743 - 746
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Copyright
© Cambridge University Press 2018 

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Footnotes

†

Current address: Department of Cardiology, Great Ormond Street Hospital for Children NHS Foundation Trust, London, United Kingdom.

References

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