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Complete tracheal rings and hypoplastic left heart variant: a rare and fatal association

Part of: Cardiac Morphology

Published online by Cambridge University Press:  24 January 2019

Neha Bansal Open the ORCID record for Neha Bansal [Opens in a new window] ,
Deemah R. Mahadin  and
Sanjeev Aggarwal
Neha Bansal*
Affiliation:
Division of Cardiology, Department of Pediatrics, Children’s Hospital of Michigan, Detroit, MI, USA
Deemah R. Mahadin
Affiliation:
Division of Cardiology, Department of Pediatrics, Children’s Hospital of Michigan, Detroit, MI, USA
Sanjeev Aggarwal
Affiliation:
Division of Cardiology, Department of Pediatrics, Children’s Hospital of Michigan, Detroit, MI, USA
*
Author for correspondence: N. Bansal, MD, Division of Cardiology, Children’s Hospital of Michigan, 3901 Beaubien Blvd, Detroit, MI 48201, USA. Tel: +1(313) 745-5481; Fax: +1 313 939 0894; E-mail: [email protected]
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Abstract

Congenital complete tracheal rings are usually associated with pulmonary slings. We report a rare association of congenital complete tracheal rings with hypoplastic left heart variant. A term infant with diagnosis of a mildly hypoplastic mitral valve, unicuspid aortic valve, and moderately hypoplastic aortic arch with severe coarctation underwent a hybrid procedure initially. Upon failing extubation attempts, complete tracheal rings were seen on direct laryngoscopy. The combination of the lesions resulted in a poor outcome. In patients with failure of extubation post-cardiac surgery, a diagnosis of complete tracheal rings should be included in the differential and a direct laryngoscopy should be considered.

Keywords

Complete tracheal ringshypoplastic left heartunicuspid aortic valve
Type
Brief Report
Information
Cardiology in the Young , Volume 29 , Issue 3 , March 2019 , pp. 445 - 447
Copyright
© Cambridge University Press 2019 

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Footnotes

Cite this article: Bansal N, Mahadin DR, Aggarwal S. (2019) Complete tracheal rings and hypoplastic left heart variant: a rare and fatal association. Cardiology in the Young29: 445–447. doi: 10.1017/S1047951118002391

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