Book contents
- Frontmatter
- Contents
- List of contributors
- Preface
- Acknowledgment
- Section 1 Head and neck
- Section 2 Thoracic imaging
- Section 3 Cardiac imaging
- Section 4 Vascular and interventional
- Section 5 Gastrointestinal imaging
- Section 6 Urinary imaging
- Section 7 Endocrine - reproductive imaging
- Section 8 Fetal imaging
- Section 9 Musculoskeletal imaging
- Case 82 Clubfoot
- Case 83 Developmental dysplasia of the hip
- Case 84 Legg–Calve–Perthes disease
- Case 85 Slipped capital femoral epiphysis
- Case 86 Langerhans cell histiocytosis: MRI/PET for diagnosis and treatment monitoring
- Case 87 Congenital syphilis
- Case 88 Medial malleolus avulsion fracture
- Case 89 Triplane fracture
- Case 90 Fibrous dysplasia
- Case 91 Chest wall sarcoma
- Case 92 Campomelic dysplasia
- Case 93 Type II collagenopathy (hypochondrogenesis)
- Case 94 Morel-Lavallée lesions
- Case 95 Infantile myofibromatosis
- Case 96 Osteochondritis dissecans of the capitellum
- Index
- References
Case 90 - Fibrous dysplasia
from Section 9 - Musculoskeletal imaging
Published online by Cambridge University Press: 05 June 2014
- Frontmatter
- Contents
- List of contributors
- Preface
- Acknowledgment
- Section 1 Head and neck
- Section 2 Thoracic imaging
- Section 3 Cardiac imaging
- Section 4 Vascular and interventional
- Section 5 Gastrointestinal imaging
- Section 6 Urinary imaging
- Section 7 Endocrine - reproductive imaging
- Section 8 Fetal imaging
- Section 9 Musculoskeletal imaging
- Case 82 Clubfoot
- Case 83 Developmental dysplasia of the hip
- Case 84 Legg–Calve–Perthes disease
- Case 85 Slipped capital femoral epiphysis
- Case 86 Langerhans cell histiocytosis: MRI/PET for diagnosis and treatment monitoring
- Case 87 Congenital syphilis
- Case 88 Medial malleolus avulsion fracture
- Case 89 Triplane fracture
- Case 90 Fibrous dysplasia
- Case 91 Chest wall sarcoma
- Case 92 Campomelic dysplasia
- Case 93 Type II collagenopathy (hypochondrogenesis)
- Case 94 Morel-Lavallée lesions
- Case 95 Infantile myofibromatosis
- Case 96 Osteochondritis dissecans of the capitellum
- Index
- References
Summary
Imaging description
A 17-year-old girl presented with progressive asymmetric left eye swelling. CT images through the left orbit demonstrated a mass centered in the left superior orbital rim, extending through the left cribriform plate and into the posterior ethmoidal air cells. The internal matrix of this mass had a ground glass appearance (Fig. 90.1a, b). The orbital apex appeared to be spared (Fig. 90.1). T2-weighted MR images through the orbit demonstrated a homogeneous hypointense signal of the mass (Fig. 90.1c, d). The mass displaced rather than invaded adjacent soft tissue structures. It displaced the frontal lobe superiorly and extended into the conus of the orbit, with mass effect on the superior and medial rectus muscles. The optic nerve did not appear to be encased. There was homogeneous enhancement of the mass on the T1-weighted MR images after intravenous administration of gadolinium (Gd)-DTPA (Fig. 90.1d). Additional CT (Figs. 90.2 and 90.3b) and plain film (Fig. 90.3a) images of two other children with fibrous dysplasia (FD), one of whom has McCune–Albright syndrome (MAS) (Fig. 90.3), demonstrate the classic ground glass bony matrix.
- Type
- Chapter
- Information
- Pearls and Pitfalls in Pediatric ImagingVariants and Other Difficult Diagnoses, pp. 365 - 369Publisher: Cambridge University PressPrint publication year: 2014